Frequency of Rare Bleeding Disorders

نویسندگان

چکیده

Objective: The incidence and range of rare hereditary bleeding diseases, as well the severity deficiency its many clinical presentations, were subjects our study. Study Design: Cross-sectional study Place Duration: Department Pathology, Northwest School Medicine Peshawar in duration from July, 2022 to December, 2022. Methods: Total 850 cases coagulation disorders presented this A thorough demographic analysis recruited was done after receiving informed written consent. After taking note symptoms indicators, a profile used diagnose patients. With use factor tests, illness evaluated. All data examined using SPSS 23.0. Results: Among cases, 113 (13.3%) patients had disorders. In disorders, there majority 70 (61.9%) males 43 (38.1%) females. Mean age 10.5±13.69 years. 47 (41.6%) urban areas 66 (58.4%) rural residency. Most common VII found 33 (29.2%) followed by fibrinogen 22 (19.5%) cases. 17 (15.04%) family history bleeding. Frequency consanguinity 88 (77.9%) symptom bruising, gum bleeding, epistaxis menorrhagia. Conclusion: We concluded higher frequency 13.3% Factor is most typical uncommon condition community. Due high rate consanguineous marriages society, these diseases are very common. Keywords: deficiency, Rare assay, Consanguinity

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ژورنال

عنوان ژورنال: Pakistan Journal of Medical and Health Sciences

سال: 2023

ISSN: ['1996-7195']

DOI: https://doi.org/10.53350/pjmhs2023174569